Priones y encefalopatías espongiformes transmisibles: un recorrido por su historia

Autores/as

  • I del C Pena

Palabras clave:

prion, encefalopatías espongiformes transmisibles, historia

Resumen

Las enfermedades causadas por priones son un grupo de enfermedades neurodegenerativas, producidas por el metabolismo aberrante de una proteína, que afectan tanto a los animales como a la especie humana. Presentan un prolongado período de incubación, alta transmisibilidad y una evolución clínica fatal y careceden de tratamiento. Se ha utilizado el término de prionpatías para denominarlas y debido a la espongiosis que producen en el sistema nervioso también se les conoce con el nombre de encefalopatías espongiformes subagudas. En este trabajo se brinda un recorrido a través de la historia de los priones, las enfermedades por ellos inducidas y las diferentes teorías que intentan explicar la etiología de estas patologías.

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2011-01-01

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Pena, . I. del C. (2011). Priones y encefalopatías espongiformes transmisibles: un recorrido por su historia. Analecta Veterinaria, 31(1), 47–60. Recuperado a partir de https://revistas.unlp.edu.ar/analecta/article/view/12208

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